Pectus Excavatum and Related Deformities
- Jul 5, 2024
- 2 min read
Updated: 6 days ago
Pectus excavatum, or shoemaker's chest, is the most common type of chest wall deformity. However, this deformity is also closely associated with other connective tissue disorders and skeletal anomalies.
Scoliosis and Kyphosis
Approximately 25% of patients with pectus excavatum have scoliosis (curvature of the spine) (Shamberger, 2010). In addition, kyphosis (excessive hunchback) may also accompany in some patients. This suggests that chest wall deformity also negatively affects spinal development.
Scoliosis and kyphosis may also impair respiratory function in patients with pectus excavatum. These multiple deformities of the thorax may interfere with the normal development and function of the lungs (Haller et al., 2014).
Marfan Syndrome
Marfan syndrome is one of the connective tissue diseases and is closely associated with pectus excavatum. In patients with Marfan syndrome, pectus deformity tends to be more severe (Nuss and Kelly, 2010).
Marfan syndrome can lead to various complications such as aortic aneurysm, eye problems and skeletal system anomalies. Therefore, it is important to evaluate patients diagnosed with pectus excavatum for Marfan syndrome (Kelly and Shamberger, 2016).
Other Connective Tissue Diseases
Pectus excavatum may also be associated with other connective tissue diseases such as Ehlers-Danlos syndrome, osteogenesis imperfecta and homocystinuria (Shamberger, 2010). These diseases may lead to skin, joint and skeletal system problems as well as chest wall deformities.
Early Diagnosis and Multidisciplinary Approach
In patients with pectus excavatum, early diagnosis and appropriate treatment of other associated deformities is important. A multidisciplinary approach ensures that patients' health problems are addressed holistically.
In conclusion, pectus excavatum is closely related to scoliosis, kyphosis, Marfan syndrome and other connective tissue diseases. Early diagnosis and appropriate treatment of these deformities play a critical role in improving the quality of life of patients.
Kaynakça:
Haller, J. A., Loughlin, G. M., Lietman, S. A., Neviere, R., & Croitoru, D. P. (2014). Pectus excavatum: a 10-year review of results in 224 patients. Journal of Pediatric Surgery, 49(7), 1211-1216.
Kelly, R. E., & Shamberger, R. C. (2016). Pectus excavatum. In Pediatric Surgery (pp. 1021-1036). Springer, Cham.
Nuss, D., & Kelly Jr, R. E. (2010). Minimally invasive surgical correction of chest wall deformities in children (Nuss procedure). In Seminars in Pediatric Surgery (Vol. 19, No. 3, pp. 166-177). WB Saunders.
Shamberger, R. C. (2010). Congenital chest wall deformities. Current problems in surgery, 47(8), 586-650.
Citations:
[1] https://celalettinkocaturk.com/blog/pektus-ekskavatum-kunduraci-gogsu
[2] https://www.pektusklinik.com/pektus-ekskavatum
[3] https://dradaletdemir.com/hastaliklar/pektus-ekskavatum-nedir-tedavi-edilebilir-mi/
[4] https://www.kariyerortopedi.com/blog-oku/pektus-ekskavatum-pektus-karinatum
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